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Published on March 1, 2016 | http://doi.org/10.5867/medwave.2016.01.6388

Neuromyelitis optica spectrum disorders as initial presentation of Sjögren's syndrome: A case report

Trastorno del espectro neuromielitis óptica como presentación inicial del síndrome de Sjögren: reporte de caso

Carlos Alva Díaz , Luis Andamayo Villalba, Nicanor Mori, Jésica Janet Ventura Chilón, Roberto Romero

Abstract

Neuromyelitis Optica Spectrum Disorder (NMOSD) is a rare systemic autoimmune disease which is sometimes found in association with other autoimmune disorders including Sjogren's syndrome. Neurological manifestations occur in 20% to 25% of diagnosed cases of Sjögren's syndrome; however, less than 5% of patients with Sjögren's syndrome have neurological manifestations as the initial presenting feature of Sjögren's syndrome. We report the case of an elderly female with longitudinal myelitis as a presenting feature who had positive antibody to aquaporin-4 (NMO-IgG) and Sjögren's syndrome.

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Authors

Carlos Alva Díaz

carlos.alexander.alva@gmail.com

Red de Eficacia Clínica y Sanitaria, Urbanización Principal 396, Distrito Surquillo, Lima, Perú

Luis Andamayo Villalba

Nicanor Mori

Jésica Janet Ventura Chilón

Roberto Romero

Servicio de Neurología, Departamento de Medicina, Hospital Daniel Alcides Carrión, Callao, Perú

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History

Citation Alva Díaz C, Andamayo Villalba L, Mori N, Ventura Chilón JJ, Romero R. Neuromyelitis optica spectrum disorders as initial presentation of Sjögren's syndrome: A case report. Medwave 2016;16(01):e6388 doi: 10.5867/medwave.2016.01.6388

Submission date 31/10/2015

Acceptance date 24/01/2016

Publication date 01/03/2016

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Keywords

Sjögren's syndrome, neuromyelitis optica spectrum disorders

Origin and peer review

con revisión por tres pares revisores externos, a doble ciego

References

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